ICD-9-CM Codes ICD-9-PCS Codes

277.5 - Mucopolysaccharidosis

GEM Conversion to ICD-10 CM

E76.01

Fs: 10000 – Hurler's syndrome

E76.03

Fs: 10000 – Scheie's syndrome

E76.1

Fs: 10000 – Mucopolysaccharidosis, type II

E76.219

Fs: 10000 – Morquio mucopolysaccharidoses, unspecified

E76.22

Fs: 10000 – Sanfilippo mucopolysaccharidoses

E76.29

Fs: 10000 – Other mucopolysaccharidoses

E76.3

Fs: 10000 – Mucopolysaccharidosis, unspecified

Sibling Codes

277.1

Disorders of porphyrin metabolism

277.2

Other disorders of purine and pyrimidine metabolism

277.4

Disorders of bilirubin excretion

277.5

Mucopolysaccharidosis

277.6

Other deficiencies of circulating enzymes

277.7

Dysmetabolic syndrome X

277.9

Unspecified disorder of metabolism