ICD-9-CM Codes ICD-9-PCS Codes

271.0 - Glycogenosis

GEM Conversion to ICD-10 CM

E74.00

Fs: 10000 – Glycogen storage disease, unspecified

E74.01

Fs: 10000 – von Gierke disease

E74.04

Fs: 10000 – McArdle disease

E74.09

Fs: 10000 – Other glycogen storage disease

E74.4

Fs: 10000 – Disorders of pyruvate metabolism and gluconeogenesis

Sibling Codes

271.0

271.1

271.2

Hereditary fructose intolerance

271.3

Intestinal disaccharidase deficiencies and disaccharide malabsorption

271.4

Renal glycosuria

271.8

Other specified disorders of carbohydrate transport and metabolism

271.9

Unspecified disorder of carbohydrate transport and metabolism