ICD-10-CM Codes Browse (Tabular) Diagnostic External Drug Neoplasm

E78.71 – Barth syndrome

Coding Notes

Active

Billable, valid for HIPAA-covered transactions

GEM Conversion to ICD-9 CM

759.89

Fs: 10000 – Other specified congenital anomalies

MDC / MS-DRG Reference

DRG 564

OTHER MUSCULOSKELETAL SYSTEM AND CONNECTIVE TISSUE DIAGNOSES WITH MCC

DRG 565

OTHER MUSCULOSKELETAL SYSTEM AND CONNECTIVE TISSUE DIAGNOSES WITH CC

DRG 566

OTHER MUSCULOSKELETAL SYSTEM AND CONNECTIVE TISSUE DIAGNOSES WITHOUT CC/MCC

Back Reference of Diagnostic Codes

Barth syndrome E78.71

Disorder (of) See also Disease

bile acid and cholesterol metabolism E78.70

Barth syndrome E78.71

cholesterol and bile acid metabolism E78.70

Barth syndrome E78.71

Syndrome See also Disease

Barth E78.71

Sibling Codes

E78.70

Disorder of bile acid and cholesterol metabolism, unspecified

E78.72

Smith-Lemli-Opitz syndrome

E78.79

Other disorders of bile acid and cholesterol metabolism

Parent Sibling Codes

View in Tabular

Code	Title
E00-E89	Endocrine, nutritional and metabolic diseases (E00-E89)
E70-E88	Metabolic disorders (E70-E88)
E78	Disorders of lipoprotein metabolism and other lipidemias
E78.7	Disorders of bile acid and cholesterol metabolism
E78.71	Barth syndrome